MARIA PILAR
GONZALEZ CABO
AYUDANTE DOCTOR/A
Argitalpenak (32) MARIA PILAR GONZALEZ CABO argitalpenak
2024
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Persistent Pulmonary Fibrotic Sequelae in Patients With Telomere Shortening One Year After Severe COVID-19
Archivos de Bronconeumologia, Vol. 60, Núm. 1, pp. 62-64
2022
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Frataxin Deficit Leads to Reduced Dynamics of Growth Cones in Dorsal Root Ganglia Neurons of Friedreich’s Ataxia YG8sR Model: A Multilinear Algebra Approach
Frontiers in Molecular Neuroscience, Vol. 15
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Therapeutic Strategies Targeting Mitochondrial Calcium Signaling: A New Hope for Neurological Diseases?
Antioxidants, Vol. 11, Núm. 1
2021
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Cofilin and neurodegeneration: New functions for an old but gold protein
Brain Sciences, Vol. 11, Núm. 7
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Friedreich Ataxia: current state-of-the-art, and future prospects for mitochondrial-focused therapies
Translational Research, Vol. 229, pp. 135-141
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PPAR gamma agonist leriglitazone improves frataxin-loss impairments in cellular and animal models of Friedreich Ataxia
Neurobiology of Disease, Vol. 148
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Role of Adenosine Receptors in Rare Neurodegenerative Diseases with Motor Symptoms
Current protein & peptide science, Vol. 22, Núm. 9, pp. 675-694
2020
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Antioxidant therapies and oxidative stress in friedreich´s ataxia: The right path or just a diversion?
Antioxidants, Vol. 9, Núm. 8, pp. 1-23
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Cofilin dysregulation alters actin turnover in frataxin-deficient neurons
Scientific Reports, Vol. 10, Núm. 1
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Much More Than a Scaffold: Cytoskeletal Proteins in Neurological Disorders
Cells, Vol. 9, Núm. 2
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Oxidative stress modulates rearrangement of endoplasmic reticulum-mitochondria contacts and calcium dysregulation in a Friedreich's ataxia model
Redox Biology, Vol. 37
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Thioredoxin and glutaredoxin systems as potential targets for the development of new treatments in Friedreich’s ataxia
Antioxidants, Vol. 9, Núm. 12, pp. 1-25
2019
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Phosphodiesterase Inhibitors Revert Axonal Dystrophy in Friedreich’s Ataxia Mouse Model
Neurotherapeutics, Vol. 16, Núm. 2, pp. 432-449
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The role of iron in Friedreich's ataxia: Insights from studies in human tissues and cellular and animal models
Frontiers in Neuroscience, Vol. 13, Núm. FEB
2017
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Circulating miR-323-3p is a biomarker for cardiomyopathy and an indicator of phenotypic variability in Friedreich's ataxia patients
Scientific Reports, Vol. 7, Núm. 1
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Reversible axonal dystrophy by calcium modulation in frataxin-deficient sensory neurons of YG8R mice
Frontiers in Molecular Neuroscience, Vol. 10
2016
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Erratum to: Guidelines for the use and interpretation of assays for monitoring autophagy (3rd edition) (Autophagy, 12, 1, 1-222, 10.1080/15548627.2015.1100356
Autophagy
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Guidelines for the use and interpretation of assays for monitoring autophagy (3rd edition)
Autophagy, Vol. 12, Núm. 1, pp. 1-222
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Two different pathogenic mechanisms, dying-back axonal neuropathy and pancreatic senescence, are present in the YG8R mouse model of Friedreich's ataxia
DMM Disease Models and Mechanisms, Vol. 9, Núm. 6, pp. 647-657
2015
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<i>Caenorhabditis elegans</i> Models to Study the Molecular Biology of Ataxias
MOVEMENT DISORDERS: GENETICS AND MODELS, 2ND EDITION (ACADEMIC PRESS LTD-ELSEVIER SCIENCE LTD), pp. 1043-1059